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KMID : 1036920120170010049
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Annals of Pediatric Endocrinology & Metabolism
2012 Volume.17 No. 1 p.49 ~ p.52
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A Case of adrenocortical oncocytoma Presenting with Peripheral Precocious Puberty
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Oh Seong-Hee
Jung Chang-Woo
Lee Jin
Lee Beom-Hee
Kim Dae-Yeon
No Dae-Yoon
Yoo Soo-Hyun
Choi Jin-Ho
Yoo Han-Wook
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Abstract
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Adrenocortical oncocytoma is a rare adrenal gland tumor, and in most cases, benign and non-functioning. Functional adrenocortical oncocytoma has only been reported in eleven cases worldwide, including three children. These cases all showed clinical symptoms and signs, such as virilization, feminization, Cushing syndrome and Conn syndrome, as a result of overproduction of adrenal steroid hormones. We report a 2-year-old girl who presented with precocious puberty with premature pubarche. Dehydroepiandrosterone sulfate (DHEA-S) and testosterone levels were elevated and a 1.9 cm right adrenocortical oncocytoma was found. After tumor resection, her hormone levels were normalized.
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KEYWORD
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Adrenocortical, Oncocytoma, Puberty, Precocious
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